Multikistik Displastik Böbrek Hastalarının Prognozları: Tek Merkez Deneyimi

Year 2024, , 1 - 6, 30.04.2024

İsa Yılmaz , Harun Peru

https://doi.org/10.47493/abantmedj.1245817

Abstract

Amaç: Bu çalışmada çocuk nefroloji kliniğimizde multikistik displastik böbrek (MKDB) saptanan hastaların demografik özellikleri ve takip sonuçlarının literatür bilgileri eşliğinde değerlendirilmesi amaçlandı.
Gereç ve Yöntemler: Ocak 2011- Ocak 2022 yılları arasında Selçuk Üniversitesi Tıp Fakültesi Çocuk Nefrolojisi kliniğine başvuran hastaların dosyaları retrospektif olarak incelendi. Multikistik displastik böbrek (MKDB) tanısı alan 21 hastanın bilgileri kaydedildi ve analiz edildi.
Bulgular: Hastaların 12’sinde (%57) sol taraflı, 9’unda (%43) sağ taraflı MKDB mevcuttu. Üriner sistem enfeksiyonu (ÜSE) üç hastada görüldü. Sağ taraflı MKDB’si olan hastaların 1’inde sağ üreterosel, 5’inde karşı böbrekte hidronefroz mevcuttu. Diğer hastalarda MKDB dışında üriner anomali izlenmedi. Hastalarda proteinüri ve hipertansiyon tespit edilmedi. İşeme sistoüretrografi çekilen 5 hastada da vezikoüreteral reflü (VUR) tespit edilmedi. Hastaların izleminde MKDB ortalama 16,2±30,07 (1-107) ayda involüsyona uğradı.
Sonuç: Çocuklarda MKDB konservatif yönetim ile iyi prognoza sahiptir. Hipertansiyon veya hiperfiltrasyon hasarının potansiyel gelişimini önlemek için periyodik takip yapılması önemlidir.

Keywords

Multikistik displastik böbrek, Sağkalım, Çocukluk çağı

Prognoses of Multicystic Dysplastic Kidney Patients: A Single Center Experience

Abstract

Objective: In this study, it was aimed to evaluate the demographic characteristics and follow-up results of patients with multicystic dysplastic kidney (MCDK) in our pediatric nephrology clinic, based on the existing medical literature.
Materials and Methods: A retrospective analysis was conducted on the medical records of patients who presented to the Pediatric Nephrology Clinic at Selçuk University Faculty of Medicine between January 2011 and January 2022. The data of 21 patients diagnosed with MCDK were recorded and analyzed.
Results: Out of the total patients, 12 (57%) had left-sided MCDK, while 10 (43%) had right-sided MCDK. Three patients experienced urinary tract infections (UTIs). Among the patients with right-sided MCDK, one had a concurrent right ureterocele, and five showed hydronephrosis in the contralateral kidney. No urinary anomalies except MCDK were observed in the remaining patients. None of the patients exhibited proteinuria nor hypertension. Vesicoureteral reflux (VUR) was not detected in the five patients who underwent voiding cystourethrography. In the follow-up of the patients, MCDK was involuted in a mean of 16.2±30,07 (1-107) months.
Conclusion: Multicystic dysplastic kidney in children has a good prognosis with conservative management. Periodic follow-up is important to prevent the potential development of hypertension or hyperfiltration injury.

Keywords

Multicystic dysplastic kidney, Survival, Childhood

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