İlk prezentasyonu otalji olan beta talasemi: olgu sunumu

Year 2015, , 174 - 177, 01.05.2015

Talih Özdaş Kürşat Murat Özcan Fatih Özdoğan Gökhan Celbek

https://doi.org/10.5505/abantmedj.2015.96967

Abstract

Beta talasemi gen mutasyonlarının sebep olduğu hematolojik bir hastalıktır ve Türkiye’yi de içeren tüm Akdeniz ülkelerinde önemli bir halk sağlığı problemi teşkil etmektedir. Talasemi intermedia talasemi major ve talasemi minor arasındaki bir ara formdur. Temporal kemik tutulumu talasemi intermediada oldukça nadirdir. Literatürde otalji ile birlikte olan ve talasemi minor tanısı alan vaka bulunmamaktadır. Bizim hastamız 10 aydır sol kulak ağrısı ve işitme kaybı çekmektedir. Bu vakada, yapılan tetkikler sonucunda talasemi intermedia tanısı alan ve manyetik rezonans görüntülemede temporal kemik tutulumu olan 44 yaşında bir erkek hasta sunulmaktadır.

Keywords

Talasemi intermedia, otalji, temporal kemik

Otalgia as the first presenting complaint in a patient with beta thalassemia: Case Report

Abstract

Beta thalassemia is a hematological disease caused by gene mutations and represents an important public health problem in all Mediterranean countries, including Turkey. Thalassemia intermedia is an intermediate form between thalassemia major and thalassemia minor. Temporal bone involvement is quite rare in thalassemia intermedia. There are no cases in the literature who presented with otalgia and was subsequently diagnosed with thalassemia intermedia. Our patient had suffered from left ear pain and hearing loss for 10 months. In this case report, a 44-year-old male patient is presented who was diagnosed with thalassemia intermedia based on the examinations performed and had temporal bone involvement on magnetic resonance imaging.

Keywords

Thalassemia intermedia, otalgia, temporal bone

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