Primer ovaryan leimyosarkom

Year 2018, Volume: 43 Issue: 4, 1038 - 1041, 29.12.2018

Gökmen Sukgen , Adem Altunkol

https://doi.org/10.17826/cumj.409817

Cited By: 2

Abstract

Over leimyosarkomu çok kötü prognozlu agresif nadir
bir tümördür. Uterin tümörlerin  aksine
ovaryan düz kas tümörleri, yumurtalık tümörlerinin sadece% 1'ini içeren çok
nadir tümörlerdir. Ovaryan leimyosarkom genellikle postmenapozal periyotta
görülür. Ancak bu vakada olduğu gibi premenapozal periyottada tanı konabilir.
Primer pür ovaryan leimyosarkomlar ovaryan düz kas hücreli tümörlerin malign
alt grubunu oluşturur. Bu nedenle kökenleri, etiyolojisi, histolojik
özellikleri, klinik davranışları ve optimal tedavileri hala belirsizdir. 59
yaşında bir hasta, karnında kitle ve ağrı şikayeti ile hastanemize başvurdu.
Ameliyat öncesi çeklen abdominal ultrasonografi ve bilgisayarlı tomografide tüm
abdomeni dolduran kitle tespit edildi.Total histerektomi, bilateral
salpingo-ooferektomi, omentektomi, appendektomi, bilateral pelvik ve paraaortik
lenf nodu diseksiyonu ve peritoneal yıkama yapıldı. Histopatolojik incelemede
primer ovaryan leimyosarkom tespit edildi. Bildiğimiz kadarıyla mevcut
vakamızla birlikte literatürde 73 vaka bildirilmiştir.

Keywords

Ovaryan neoplasm, sarkom, leimyosarkom

Primary leimyosarcoma of the ovary

Abstract

Ovarian leimyosarcoma is a rare aggressive tumor with a very bad prognosis. Contrary to their uterine counterparts, ovarian smooth muscle tumors are extremely rare comprising only 1% of ovarian tumors. Ovarian leimyosarcoma is generally seen in the postmenopausal period. Here we report a 59-year old patient diagnosed as  as ovarian primary leimyosarcoma. 

Keywords

Ovarian neoplasm, sarcoma, leimyosarcoma

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