Sex-cord stromal tumour with annular tubules of the ovary without Peutz-Jeghers Syndrome: A case report

Year 2020, Volume: 2 Issue: 4, 143 - 145, 28.12.2020

Ediz Karataş Dilek Yüksel , Çiğdem Kılıç , Caner Çakır , Onur Şahin Mehmet Ünsal , Çiğdem Mesci Taner Turan

https://doi.org/10.46969/ezh.710577

Abstract

Annular tubules sex-cord tumours constitute a rare subtype of sex-cord stromal tumours. Clinical features depend on
concomitance with Peutz-Jeghers Syndrome (PJS). The type, not associated with PJS, presents with malignancy at a rate
of 20%. The present article aimed to present the case of a 22-year-old primary infertile patient with malignant annular
tubules sex-cord stromal tumour without PJS.

Keywords

Sex-cord stromal tumour with annuler tubules, Peutz-Jeghers Syndrome, Ovarian neoplasm

Peutz-Jeghers sendromu ile ilişkili olmayan overin malign annüler tubuli seks-kord stromal tümörü: Olgu sunumu

Abstract

Annüler tubuli seks-kord tümörler seks kord stromal tümörlerin nadir bir alt tipidir. Klinik özellikleri Peutz-Jeghers
Sendromu (PJS) ile birlikte olup olmamasına bağlıdır. PJS ile ilişkili olmayan tip %20 oranında malignite ile seyretmektedir.
Bu makalede 22 yaşında, primer infertil, PJS’nun eşlik etmediği malign annüler tubuli seks-kord stromal tümör olgusunun
sunulması amaçlanmıştır.

Keywords

Annüler tubuli sex-kord stromal tümör, Peutz-Jeghers Sendromu, ovarian neoplazm

References

• Thrall MM, Paley P, Pizer E, Garcia R, Goff BA. Patterns of spread and recurrence of sex cord- stromal tumors of the ovary. Gynecol Oncol 2011; 122:242-245.
• Scully RE, Sobin LH. Histological typing of ovarian tumors. Arch Pathol Lab Med 1987; 111:794-795.
• Mangili G, Taccagni G, Garavaglia E, Carnelli M, Montoli S. An unusual admixture of neoplastic and metaplastic lesions of the female genital tract in the Peutz Jeghers Syndrome. Gynecol Oncol 2004; 92:337-342.
• Barker D, Sharma R, Mclndoe A, et al. An unusual case of sex cord tumor with annular tubules with malignant transformation in a patient with Peutz Jeghers Syndrome. Int J Gynecol Pathol 2010; 29:27-32.
• Kondi-Pafiti A, Bakalianou K, Lavazzo C, Dastamani C,Hasiakos D, Liapis A. Endometrial carcinoma and ovarian sex cord tumor with annular tubules in a patient with history of Peutz-Jeghers Syndrome and multipl malignancies. Eur J Gynaecol Oncol 2011; 32:452-454.
• Aslan F, Akkaş G. Peutz Jeghers Sendromu Olmayan Olguda Overde Bilateral Anüler Tubuluslu Seks Kord Tümör: Olgu sunumu. Kocatepe Tıp Dergisi 2014; 15:68-73.
• Shen K, Wu PC, Lang JH, Huang RL, Tang MT, Lian LJ. Ovarian sex cord tumor with annular tubules: A report of six cases. Gynecol Oncol 1993; 48:180-184.
• Momin YA, Kulkarni MP, Pandav AB, Sulhyan KR. Non Peutz-Jegher Syndrome associated malignant sex cord stromal tumor with annular tubules. Int J Appl Basic Med Res 2013; 3:126-128.
• Puls LE, Hamous J, Morrow MS, Schneyer A, Maclaughlin DT, Castracane VD. Recurrent ovarian sex cord tumor with annular tubules: tumor marker and chemotherapy experience. Gynecol Oncol 1994; 54:396-401.
• Qian Q, You Y, Yang J, et al. Management and prognosis of patients with ovarian sex cord tumor with annuler tubules: a retrospective study. BMC Cancer 2015; 15:270.