Class I pentalogy of Cantrell: a rare case report

Year 2017, Volume: 3 Issue: 1, 83 - 86, 04.03.2017

Bayram Ali Dorum , Hilal Ozkan , Nilgun Koksal , Yasemin Denkboy Ongen

https://doi.org/10.18621/eurj.293251

Abstract

Pentalogy of Cantrell is characterized by the presence of five major congenital defects involving the abdominal wall, pericardium, diaphragm, lower sternum and various cardiac abnormalities. This rare syndrome was described by Cantrell in 1958 and it has poor prognosis. We report here a case of class I Cantrell syndrome and our aim is to share difficulties experienced and review the related literature.

Keywords

Cantrell syndrome, ectopia cordis, omphalocele, ventricular diverticulum

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