Periaortitli Hastada Retroperitoneal ve Mediastinal Fibrozis Birlikteliği: Olgu Sunusu

Year 2017, Volume: 14 Issue: 1, 75 - 80, 28.04.2017

Mustafa Reşorlu , Canan Akgün Toprak Muhsin Özgün Öztürk

Abstract

Kronik periaortit daha sık orta yaş erkekleri etkilemekte ve nadir olarak görülmektedir. Patofizyolojisinde
otoimmünitenin etkili olduğu ve idiopatik retroperitoneal fibrozis, perianevrizmal fibrozis, enflamatuar
abdominal aort anevrizması ile ilişkili olduğu ileri sürülmektedir. Retroperitoneal fibrozis olgularının büyük
kısmı idiopatiktir. Mediastinal fibrozis ise sıklıkla enfeksiyoz süreçle ilişkilidir. Bu iki patolojik tablonun
birlikteliği ise oldukça nadirdir. Biz bu çalışmamızda periaortiti olan bir hastamızda eşlik eden
retroperitoneal ve mediastinal fibrozis birlikteliğini sunmayı amaçladık 

Keywords

Retroperitoneal fibrozis, mediastinal fibrozis, periaortit

Comorbid Retroperitoneal and Mediastinal Fibrosis in a Case of Periaortitis

Abstract

Chronic periaortitis is a rare condition. Middle-aged males comprise a large proportion of patients. An
association has been proposed with idiopathic retroperitoneal fibrosis, perianeurysmal fibrosis and
inflammatory abdominal aortic aneurysm, and autoimmunity has been implicated in the pathophysiology.
Comorbidity of retroperitoneal fibrosis, which is frequently idiopathic, and mediastinal fibrosis, which is
particularly associated with infectious processes, is rare. The purpose of this study was to report a case
of comorbid retroperitoneal and mediastinal fibrosis in a patient with periaortitis, together with imaging
findings

Keywords

Retroperitoneal fibrosis, Mediastinal fibrosis, Periaortitis

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