Clinical, Demographic and Echocardiographic Characteristics Of Pediatric Chest Deformities

Year 2023, Volume: 13 Issue: 2, 360 - 364, 22.03.2023

Melih Timuçin Doğan , Ahmet Sert

https://doi.org/10.16899/jcm.1221665

Cited By: 1

Abstract

Objective: We aimed to retrospectively evaluate the clinical, demographic, clinical and echocardiographic findings of children diagnosed with chest deformity in the pediatric cardiology clinic.
Material and Method: This study enrolled children under the age of 18 years who were referred with chest deformity to our pediatric cardiology unit, over a period of six years (January 2017-December 2022).
Results: The mean age of the patients was 9.9 ± 5.2 years, median 11 years (0-18 years old). 89 patients with abnormal echocardiographic findings: 42 (9.56%) mitral valve prolapse, 18 (4.1%) atrial septal defect, 9 (2%) ventricular septal defect, 8 (1.82%) bicuspid without aortic valve stenosis aortic valve, 5 (1.1%) patent ductus arteriosus, 2 (0.45%) pulmonary stenosis, 2 (0.45%) great artery transposition, 2 (0.45%) hypertrophic cardiomyopathy, subaortic ridge 1 (% 0.27). Cardiac compression was present in 13.4% of the cases with pectus excavatum. 13(%3) patients were operated by a thoracic surgeon. Marfan Syndrome was diagnosed in 7 patients and Noonan Syndrome was diagnosed in 2 patients who applied to our clinic with chest deformity.
Conclusion: We suggest that echocardiographic examination in patients with chest deformity is important in the diagnosis of congenital heart diseases, early diagnosis and treatment of heart compression finding.

Keywords

children, chest deformity, echocardiography

Pediatrik Göğüs Deformitelerinin Klinik, Demografik ve Ekokardiyografik Özellikleri

Abstract

Amaç: Çocuk kardiyoloji kliniğinde göğüs deformitesi tanısı alan çocukların klinik, demografik, klinik ve ekokardiyografik bulgularını retrospektif olarak değerlendirmeyi amaçladık.
Gereç Ve Yöntem: Bu çalışmaya altı yıl boyunca (Ocak 2017-Aralık 2022) pediatrik kardiyoloji birimimize göğüs deformitesi ile başvuran 18 yaş altı çocuklar dahil edildi.
Bulgular: Hastaların yaş ortalaması 9,9 ± 5,2 median:11 yaş (0-18 yaş) idi. Anormal ekokardiyografik bulguları olan 89 hasta: 42 (%9,56) mitral kapak prolapsusu, 18 (%4,1) atriyal septal defekt, 9 (%2) ventriküler septal defekt, 8 (%1,82) aort kapak darlığı olmayan biküspid aort kapak, 5 (%1,1) patent duktus arteriozus, 2 (%0,45) pulmoner darlık, 2 (%0,45) büyük arter transpozisyonu, 2 (%0,45) hipertrofik kardiyomiyopati, subaortik ridge 1 (%0,27) idi. Pektus ekskavatumlu olguların %13.4'ünde kardiyak bası vardı. 13(%3) hasta göğüs cerrahisi tarafından opere edildi. Göğüs deformitesi ile kliniğimize başvuran 7 hastada Marfan Sendromu, 2 hastada Noonan Sendromu teşhis edildi.
Sonuç: Göğüs deformitesi olan hastalarda ekokardiyografik incelemenin doğumsal kalp hastalıklarının tanısında, kalp sıkışması bulgusunun erken tanı ve tedavisinde önemli olduğunu düşünüyoruz.

Keywords

çocuklar, göğüs deformitesi, ekokardiyografi

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