A Rare Cause of Abdominal Pain: Herlyn-Werner- Wunderlich Syndrome

Year 2023, , 87 - 90, 31.12.2023

Fatih Mehmet Aksoy , Erdal Yavuz , Kasım Turgut , Umut Gülaçtı , İrfan Aydın

https://doi.org/10.33706/jemcr.1333411

Abstract

Herlyn-Werner-Wunderlich (HWW) syndrome is a congenital urogenital syndrome. Typical features are unilateral blind-ending hemivagina with uterine didelphy and ipsilateral renal agenesis. Patients usually progress asymptomatically until menarche, and they are diagnosed with radiological imaging by applying to the hospital with these conditions such as abdominal pain, abdominal bloating, primary amenorrhea along with menarche. In this case report, it is aimed to present a patient who applied to our emergency department with abdominal pain and is diagnosed with HWW syndrome. In this case, it is emphasized that emergency physicians should regard to HWW syndrome in the differential diagnosis of abdominal pain.

Keywords

Keywords: Herlyn-Werner-Wunderlich, Müllerian Anomaly, Abdominal Pain

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