Effect of pulmonary rehabilitation on adult cystic fibrosis patient: a case report

Year 2019, Volume: 6 Issue: 3, 220 - 225, 10.01.2020

Gamze Yalçınkaya , Aylin Özgen Alpaydın , Sevgi Özalevli

Abstract

Cystic fibrosis
is an autosomal recessive and fatal disease that affect the respiratory
functions and daily living activities of patients. Fifty percent of the cystic
fibrosis population consists of adult patients aged 18 years and older. The
most common problems are decreased pulmonary function and exercise capacity in
adult cystic fibrosis. In addition, many different comorbidities can be seen
such as diabetes, osteoporosis and pain due to systematic influence. Pulmonary
rehabilitation is known to increase mucus clearance and exercise tolerance in
adult cystic fibrosis patients, however the studies that investigating the
effectiveness of pulmonary rehabilitation are limited in this population.  Therefore, pulmonary rehabilitation program
of an adult patient with cystic fibrosis was performed in our study. The
patient was included in an 8-week supervised pulmonary rehabilitation program
with two sessions per week. The patient's severity of dyspnea perception,
pulmonary function test, cardiopulmonary exercise test, static stabilization of
the trunk muscles, quadriceps muscle strength, grip strength and health-related
quality of life were assessed before and after the pulmonary rehabilitation
program. Breathing exercises, bronchial hygiene techniques, aerobic training
and home program were applied to our patient within the scope of pulmonary
rehabilitation program. The patient's severity of dyspnea perception was
decreased while 6-minute walking distance, cardiopulmonary exercise test
parameters and respiratory function test results increased at the end of the
8-week supervised pulmonary rehabilitation program. The patient’s grip strength
and static trunk endurance increased while the quadriceps muscle strength did
not change. In addition, it was determined that the patient’s quality of life
increased according to the Saint George Respiratory Questionnaire.

Keywords

Cystic fibrosis, Pulmonary Rehabiltation, Exercise

Pulmoner rehabilitasyonun erişkin kistik fibrozisli hasta üzerindeki etkisi: bir olgu sunumu

Abstract

Kistik fibrozis otozomal resesif geçişli,
hastaların solunum fonksiyonları ve günlük yaşam aktivitelerini etkileyen
ölümcül bir hastalıktır. Kistik fibrozisli popülasyonun %50’si 18 yaş ve üzeri
erişkin hastalardan oluşmaktadır. Erişkin kistik fibroziste en yaygın görülen
problemler solunum fonksiyonları ve egzersiz kapasitesinin azalmasıdır. Ek
olarak, sistematik etkilenimden dolayı diyabet, osteoporoz ve ağrı gibi birçok
farklı problem de görülebilmektedir. Erişkin kistik fibrozisli hastalarda
pulmoner rehabilitasyonun mukus klirensini ve egzersiz toleransını artırdığı
bilinmektedir ancak bu popülasyonda pulmoner rehabilitasyonun etkinliğini
araştıran yayınlar sınırlı sayıdadır. Bu nedenle, çalışmamızda kistik
fibrozisli erişkin bir hastanın pulmoner rehabilitasyon programı
gerçekleştirildi. Hasta, haftada iki seans olacak şekilde 8 haftalık hastaya
özgü planlanmış bir pulmoner rehabilitasyon programına dahil edildi.
Programının öncesinde ve sonrasında hastanın dispne seviyesi, solunum fonksiyon
testi, kardiyopulmoner egzersiz testi, gövde kaslarının statik stabilizasyonu,
quadriceps kas kuvveti, kavrama kuvveti ve sağlıkla ilişkili yaşam kalitesi
değerlendirildi. Pulmoner rehabilitasyon programı kapsamında hastamıza solunum
egzersizleri, bronşiyal hijyen teknikleri, aerobik eğitim ve ev programı
uygulandı. 8 haftalık pulmoner rehabilitasyon programı sonunda hastanın 6
dakika yürüme mesafesi, kardiyopulmoner egzersiz testi parametreleri ve solunum
fonksiyon test sonuçları artarken, algılanan dispne şiddeti azaldı. Hastanın
quadriceps kas kuvvetinde tedavi başlangıcına göre değişim görülmezken, kavrama
kuvveti ve statik gövde enduransı arttı. Ek olarak, Saint George Solunum
Anketi’ne göre hastanın yaşam kalitesinin arttığı belirlendi. 

Keywords

Kistik fibrozis, pulmoner rehabilitasyon, egzersiz

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