Congenital Cystic Adenomatoid Malformation As A Rare Cause Of Respiratory Distress In Newborn

Year 2013, Volume: 10 Issue: 38, 1602 - 1603, 01.04.2013

Nurdan Fettah Dilek Dilli , Nuran Uzunalıç Ayşegül Zenciroğlu Nurullah Okumuş İbrahim Karaman

Abstract

Congenital cystic adenomatoid malformation CCAM is a rare lung disorder developed as a result of the improper fusion of the bronchial buds with the alveolar mesenchyme during embryological development. Depending on the type of lesion, CCAM tissue pressure in newborns may cause respiratory distress and may later manifest itself as recurrent pulmonary infections in young adults. Lobectomy has been recommended in symptomatic. patients; whereas surgical intervention may be delayed in asymptomatic patients for 6-12 months.

Keywords

Congenital Cystic Adenomatoid Malformation, Newborn, Lung, Lobectomy, Respiratory Distress

Yenidoğanda Nadir Bir Solunum Sıkıntısı Nedeni: Konjenital Kistik Adenoid Malformasyon

Abstract

Konjenital kistik adenoid malformasyon KKAM bronşiyal tomurcukların alveolar mezenşimle uygun şekilde birleşememesi sonucu ortaya çıkan akciğerin nadir görülen embryolojik gelişim bozukluğudur. Lezyonun tipine göre, KKAM fonksiyon gören pulmoner dokuya bası ile yenidoğanlarda solunum güçlüğüne yol açabilir veya genç erişkinde rekürren akciğer enfeksiyonu ile kendini gösterebilir. Semptomatik olgularda lobektemi önerilmekte, asemptomatik olgularda ise 6-12 aya kadar girişimin geciktirilebileceği bildirilmektedir.

Keywords

Konjenital Kistik Adenomatoid Malformasyon, Yenidoğan, Akciğer, Lobektomi, Respiratuvar Distress

References

• Avitabile AM, Greco MA, Hulnick DH, Feiner HD: Congenital cystic adenomatoid malformation of the lung in adults. Am J Surg Pathol “1984:193-202, 2) Revillon Y, Jan D, Plattner V, et al. Congenital cystic adenomatoid malformation of the lung: prenatal management and prognosis. J Pediatr Surg 1993; 28:1009-11.
• Stocker JT, Madewell JE, Drake RM: Congenital cystic adenomatoid malformation of the lung. Classification and morphologic spectrum. Hum Pathol 1977; 8:155-71.
• Thorpe-Beeston JG, Nicolaides KH. Cystic adenomatoid malformation of the lung: prenatal diagnosis and outcome. Prenatal Diagnosis 1994; 14:677-88
• May DA, Barth RA, Yeager S, Nussbaum-Blask A, Bulas DI. Perinatal and postnatal chest sonography. Radiol Clin North Am1993; 31:499-516.
• Sapin E, Lejeune V, Barbet JP, et al. Congenital adenomatoid disease of the lung: prenatal diagnosis and perinatal management. Pediatr Surg Int 1997; 12:126-9.