Myelit bulguları ile prezente olan ve sicca semptomları olmayan sjögren vakası

Year 2017, , 89 - 91, 15.07.2017

Şeyda Bayil , Hacer Erdem Tilki

https://doi.org/10.30565/medalanya.294029

Abstract

Sjögren sendromu (SS) egzokrin bezlerin kronik, inflamatuar ve
otoimmün hastalığıdır. SS' da hastaların %20' sinde nörolojik bulgular gelişir.
Nörolojik bulgular göz ve ağız kuruluğu gibi sicca semptomları ortaya çıkmadan
önce de görülebilir. Periferik sinir sistemi tutulumu (PSS) %15, santral sinir
sistemi (SSS) tutulumu %5 oranında görülür. SSS tutulumu, PSS tutulumuna göre
çok daha az görülür. Bu vakada, transvers myelit ile prezente olan, serum anti
Ro-SSA/anti La-SSB antikorları negatif olan ve sicca bulguları olmayan bir
sjögren sendromu ele alınmıştır.

Keywords

Sjögren sendromu, Myelit, Sicca semptomları

A Sjögren's syndrome case presenting with myelitis and without sicca symptoms

Abstract

Sjögren’s syndrome (SS) is a chronic inflammatory disorder of exocrine
glands with autoimmune etiology. Neurological symptoms occur in approximately
20% of patients with Sjögren’s syndrome. 
Neurological symptoms may occur before the onset of sicca symptoms such
as; dry eyes and dry mouth. The prevalence of peripheral and central
neurological manifestations in  Sjögren
syndrome are about 15% and 5% respectively. CNS involvement is much less common
than peripheral nervous system involvement. In this case, our patient presented
symptoms of transverse myelitis; however, the serum Anti-Ro/SSA and anti-La/SSB
antibodies were negative and there were no dry eyes and dry mouth.

Keywords

Sjögren’s syndrome, Myelitis, Sicca symptoms

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