Falanks Enkondromunun Osteopoıkılozlu Kemikten Alınan Otogreft ile Tedavisi: Olgu Sunumu

Year 2017, Volume: 1 Issue: 2, 92 - 95, 15.07.2017

Gökhan Peker , Sunkar Kaya Bayrak Alkan Bayrak , Dila Mete Peker

https://doi.org/10.30565/medalanya.312149

Cited By: 1

Abstract

Osteopoikiloz, çocukluk çağında gelişmeye başlayan ve ileri
yaşlarda devam eden, enkondral kemik matürasyonunda anormallikle karakterize,
nadir görülen bir kemik displazisidir. 
Sıklıkla asemptomatik olmakla beraber genellikle rastlantısal olarak
saptanır. Otozomal dominant geçişli olan patoloji, sporadik olarak da
görülebilmektedir. Enkondrom ise klasik olarak hiyalin kıkırdak kökenli benign,
ayak ve el kemikleri gibi küçük kemiklerde yerleşmiş olan uzunlamasına ve oval
kemik lezyonlarıdır. Bu çalışmamızda, osteopoikiloz tanılı ve falanksında
enkondrom oluşan olgumuzu sunmayı ve tedavisini tartışmayı amaçladık. 

Keywords

osteopoikiloz, enkondrom, falanks

Treatment Of Phalanx Enchondroma By Autograft Harvested From The Bone With Osteopoikilosis: A Case Report

Abstract

Osteopoikilosis is a rare bone dysplasia characterized by
abnormally enchondral bone maturation, which generally stars to be formed in
the childhood and continues in the adulthood. It is generally asemptomatic and
it is determined incidentally. As it is generally inherited otosomal
dominantly, sporadic cases can also be seen. Enchondroma is a benign lesion
formed from hyaline cartilage mostly in small bones like foot and hand with
longitudinal and elliptic shape. In this study, we would like to discuss the
patient with phalangeal enchondroma and osteopoikilosis.

Keywords

osteopoikilosis, enchondroma, phalanx

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