Idiopatic Infantile Arterial Calcification: Echocardiography Diagnosis and Successful Treatment

Year 2019, Volume: 2 Issue: 1, 27 - 28, 15.10.2019

Hasan Onal , Neval Topal Melek Yıldız Banu Aydın Aygün Dindar

Abstract

Idiopathic
infantile arterial calcification is
rare disease characterized by medial calcification and intimal proliferation of
large and medium size arteries (1).

Prenatal prezantation is usually with nonimmune
hidrops and polyhydamnios (2). Although the clinical characteristics in
neonatal period is variable, respiratory distress with cardiac failure is the
most common finding. Hypertension due to poor compliance caused by diffuse
arterial calcification of the vessels is present in most patients.

Clinical experience in treating this rare disorder is
limited. We present a neonatal case with Idiopathic infantile
arterial calcification
who was treated with etidronate disodium, successfully.

Keywords

Arterial Calcification

References

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