A Rare Case: VACTERL Asociation in a Newborn

Yıl 2025, Sayı: 3, 145 - 149, 14.03.2025

Talha Ceran , Şeyda Gökalp , Nuriye Tarakçı , Hüseyin Altunhan , Canan Kocaoğlu

https://doi.org/10.70846/nigdetip.1559680

Öz

VACTERL association; It is a clinical condition in which at least three of the following vertebral, anorectal, cardiac, tracheoesophageal, renal and extremity anomalies occur together. It was determined as 1/10000-1/40000. Its etiology has not been specifically defined and the diagnosis is made based on clinical findings. In this article, we wanted to present a newborn case with tracheoesophageal fistula, esophageal atresia, anal atresia and left kidney hydronephrosis, which we diagnosed as VACTERL association, which is clinically rare.

Anahtar Kelimeler

Tracheoesophageal fistula, esophageal atresia, anal atresia, hydronephrosis, VACTERL association

Nadir Görülen Bir Olgu: Yenidoğanda VACTERL Asosiasyonu

Öz

VACTERL asosiasyonu; vertebral, anorektal, kardiyak, trakeoözafagial, renal ve ekstremite anomalilerinden en az üç tanesinin bir arada görüldüğü klinik durumdur. 1/10000-1/40000 oranında saptanmıştır. Etiyolojisi spesifik olarak tanımlanmamıştır ve tanı klinik bulgulara dayanarak konur. Biz bu makalede trakeoözofagial fistül, özefagus atrezisi, anal atrezi ve sol böbrekte hidronefrozu olan klinik olarak nadir görülen VACTERL asosiasyonu tanısını koyduğumuz yenidoğan olgusunu sunmak istedik.

Anahtar Kelimeler

Trakeoözafagial fistül, özefagus atrezisi, anal atrezi, hidronefroz, VACTERL asosiasyonu

Kaynakça

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