A Different Clinical Presentation for Intestinal Obstruction due to Rapunzel Syndrome: Diarrhea

Year 2021, Volume: 6 Issue: 1, 143 - 149, 05.03.2021

Aytaç Taşcı , Turan Yıldız

https://doi.org/10.26453/otjhs.844272

Abstract

Trichobezoars are defined as accumulation of hair or hair like substances in the stomach and/or small intestinal. It’s called Rapunzel syndrome when the accumulated hair ball pass the pylorus and reaches the small intestines and colon from the stomach. Clinical findings and treatment methods may vary according to the localization and size of the hair ball. In the literature; there are a limited of number publications about trichobezoar and Rapunzel syndrome but there hasn’t been a report of intestinal obstruction due to trichobezoar presenting to the emergency department with diarrhea. In this report; we will present a patient who applied to the emergency department with diarrhea and vomiting associated with intestinal obstruction due to Rapunzel syndrome.

Keywords

Rapunzel syndrome, trichobezoars,, intestinal obstruction

Rapunzel Sendromuna Bağlı İntestinal Obstrüksiyonun Farklı Bir Klinik Sunumu: İshal

Abstract

TTrikobezoar yutulan saç veya saç benzeri maddelerin mide ve/veya ince barsakda birikimine denilir. Midede biriken saç topunun nadiren de olsa piloru geçerek ince barsaklara hatta kolona ulaşmasına Rapunzel sendromu denilmektedir. Klinik bulgular ve tedavi yöntemleri saç topunun büyüklük ve konumuna göre değişmektedir. Literatürde trikobezoarlar hakkında sınırlı sayıda yayın olmak ile beraber trikobezoar nedeniyle gelişen intestinal obstrüksiyon sonrası ishal ile acil servise başvuru hakkında yayın yoktur. Yazımızda acil servisimize Rapunzel sendromuna bağlı intestinal obstrüksiyon sonrası ishal ve kusma ile başvuran bir hastayı sunacağız.

Keywords

Rapunzel sendromu,, trikobezoar,, intestinal obstrüksiyon

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