A Rare Presentation of Aortic Coarctation: Distal Thoracic Aortic Coarctation: A Case Report

Year 2020, Volume: 8 Issue: 3, 105 - 108, 25.12.2020

Ahmet Sert , Nezire Yılmaz , Mustafa Koplay

Abstract

Congenital aortic coarctation is mostly defined as a segmental narrowing that develops in the area where the ductus arteriole is attached to the aorta. Middle aortic syndrome, which is a rare variant is the form of aortic coarctation where the distal thoracic aorta or the abdominal aorta or both. Most cases arise from segmental or diffuse narrowing of the abdominal and / or distal descending thoracic aorta with variable involvement of the renal and visceral branches. Hypertension and claudication usually occur children with distal thoracic aortic coarctation. In case report, a 5-year-old girl presented with leg pain was diagnosed as distal thorasic aortic coarctation. It was presented for rarely seen in literature.

Keywords

Congenital coarctation of the thoracic aorta, hypertension, claudication

Aort Koarktasyonunun Nadir Bir Prezentasyonu: Distal Torasik Aort Koarktasyonu: Olgu Sunumu

Abstract

Aort koarktasyonu çoğunlukla duktus arteriyosuzun aortaya tutunduğu bölgede gelişen segmental bir daralma olarak tanımlanmaktadır. Aort koarkasyonunun nadir rastladığımız bir varyantı olan middle aortik sendrom; aort koarktasyonunun distal torasik aorta veya abdominal aorta veya her ikisinin birlikte bulunduğu şeklidir. Olguların çoğu, renal ve visseral dalların değişken
tutulumu ile birlikte, abdominal ve/veya distal inen torasik aortanın segmental veya yaygın daralmasıyla ortaya çıkmaktadır. Distal torasik aort koarktasyonunda çocuklarda genellikle hipertansiyon ve kladikasyon ortaya çıkar. Bu yazıda bacak ağrısıyla prezente olan 5 yaşında kız hastaya distal torasik aort koarktasyonu tanısı konuldu. Literatürde nadir görüldüğü için sunulmuştur.

Keywords

Konjenital torasik aort koarktasyonu, hipertansiyon, kladikasyon

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