Intraabdominal Synovial Sarcoma, A Rare Tumour and Rare Localisation

Year 2018, Volume: 8 Issue: 3, 669 - 673, 30.09.2018

Mustafa Yener Uzunoğlu , Fatih Altıntoprak , Enis Dikicier , Zeynep Kahyaoğlu

https://doi.org/10.31832/smj.404264

Abstract

Synovial
sarcomas are often seen in the soft tissues, intra-abdominal synovial sarcomas
are extremely rare. An intra-abdominal mass starting from the umbilicus and
extending into the pelvis was detected in a 53-year-old man admitted with
abdominal pain and a palpable mass. Total mass excision surgery was performed
and the mass was found to be an intra-abdominal synovial sarcoma arise from
small bowel wall histopathologically. Unfortunately, this is a malignancy with
a poor prognosis and a short survival despite all therapeutic efforts

Keywords

intra-abdominal mass, sarcoma, small bowel wall

Intraabdominal Sinovyal Sarkom, Nadir Lokalizasyonda Nadir Bir Tümör

Abstract

Sinovyal
sarkomlar sıklıkla yumuşak dokuda gözlenirler, intra abdominal sinovyal
sarkomlar oldukça nadirdir. Karın ağrısı ve palpabl kitle ile başvuran 53 yaşında
erkek bir hastada umbilikustan başlayıp, pelvise kadar uzanım gösteren karın içi
kitle saptandı. Total kitle eksizyonu yapılan hastada, histopatolojik olarak
ince barsak duvarından kaynaklanan intraabdominal sinovyal sarkom bulundu. Ne
yazık ki, bu malignite zayıf prognoza sahiptir ve yapılan tüm tedavilere rağmen
sağkalımı kısadır.

Keywords

ince barsak duvarı, intraabdominal kitle, sarkom

References

• 1)Sultan I, Rodriguez-Galindo C, Saab R, Yasir S, Casanova M, Ferrari A. Comparing children and adults with synovial sarcoma in the Surveillance, Epidemiology, and End Results program, 1983 to 2005. Cancer 2009; 115: 15, 3537–3547 DOI: 10.1002/cncr.24424
• 2) Ko SF, Chou FF, Huang CH, Ng SH, Wan YL, Lee TY et al. Primary Synovial Sarcoma Of The Gastrocolic Ligament The British Journal Of Radiology1998; 438-440 DOI: 10.1259/bjr.71.844.9659138
• 3)Carrillo R, Rodriguez-Peralto JL, Batsakis JG. Synovial sarcoma of the head and neck. Ann Otol Rhinol Laryngol. 1992 Aprİ; 101(4):367-70. DOI: 10.1177/000348949210100415
• 4)Fritsch M, Epstein JI, Perman EJ, Watts JC, Argani P. Molecularly confirmed primary prostatic synovial sarcoma. Hum Pathol 2000; 31:246-250 DOI: https://doi.org/10.1016/S0046-8177(00)80228-2
• 5)Fisher C, Folpe AL, Hashimoto H, Weiss SW. Intra-abdominal synovial sarcoma: a clinicopathological study. Histopatology September 2004; Volume 45, Issue 3, pages 245–253 DOI: 10.1111/j.1365-2559.2004.01950.x
• 6)Buiga-Potcoavă R, Crişan D, Olinici CD. Primary intraabdominal sarcoma, a case report Romanian Journal Of Gastroenterology March 2005; Vol.14 No.1 67-69
• 7)Harsh KK, Kalwar A, Kapoor A, Jakhar SL, Kumar HS. Giant cell variant of malignant fibrous histiocytoma of male breast: A rare case report. J Can Res Ther 2015;11:657 DOI: 10.4103/0973-1482.138129
• 8)Changchien YC, Katalin U, Fillinger J, Fónyad L, Papp G, Salamon F, Sápi Z. A Challenging Case of Metastatic Intra-Abdominal Synovial Sarcoma with Unusual Immunophenotype and Its Differential Diagnosis. Case Rep Pathol. 2012; 2012: 786083. DOI: 10.1155/2012/786083.
• 9)Eriksen C, Burns L, Bohlke A, Haque S, Slakey DP. Management of monophasic synovial sarcoma of the small intestine. JSLS. 2010;14(3):421-5. DOI: 10.4293/108680810X12924466006846.
• 10)Guillou L, Coindre JM, Gallagher G, Terrier P, Gebhard S, Somerhausen NSA, et al. Detection of the synovial sarcoma translocation t(X;18) (SYT;SSX) in parafin-embedded tissues using reverse transcriptasepolymerase chain reaction: a reliable and powerful diagnostic tool for pathologist. A molecular analysis of 221 mesenchymal tumors fixed in different fixatives. Hum Pathol 2001; 32:105-112. DOI: https://doi.org/10.1053/hupa.2001.21130