Ailevi Akdeniz Ateşi Olan 2-18 Yaş Arası Çocuklarda Sağlıkla İlişkili Yaşam Kalitesinin Değerlendirilmesi

Year 2022, Volume: 16 Issue: 6, 469 - 475, 30.11.2022

Sevgi Yaşar Durmuş , Sare Gülfem Özlü , Esra Çöp , Mehmet Bülbül

https://doi.org/10.12956/tchd.1013742

Cited By: 2

Abstract

Amaç: Bu çalışmada ailevi Akdeniz ateşi (AAA) olan 2-18 yaş arası çocuk hastaların ve ebeveynlerinin sağlıkla ilgili yaşam kalitesini değerlendirmek ve aynı yaş grubundaki sağlıklı çocuklar ile karşılaştırmak amaçlandı.

Gereç ve Yöntemler: Ailevi Akdeniz ateşi olan 51 çocuk ile yaş ve cins olarak eşleştirilmiş 51 sağlıklı gönüllü çalışmaya dahil edildi. Sekiz-18 yaş arası çocuklar PedsQL4.0 çocuk formunu doldururken, tüm yaş gruplarında ebeveynler PedsQL4.0 ebeveyn formunu doldurdu.

Bulgular: Sekiz-18 yaş grubu çocuk formlarının değerlendirilmesinde, istatistiksel anlamlı olmamakla birlikte, fiziksel sağlık, sosyal sağlık, okul işlevselliği, psikososyal total skor ve ölçek toplam skoru açısından AAA olan çocukların puanlarının daha düşük olduğu saptandı.
Ebeveyn PedsQL4.0 değerlendirildiğinde ise tüm yaş gruplarında AAA olan çocukların ebeveynlerinde fiziksel, duygusal, sosyal, psikososyal, okul işlevselliği skorları ve ölçek toplam skorlarının sağlıklı çocukların aileleri ile karşılaştırıldığında daha düşük olduğu ancak istatistiksel anlamlı düzeye ulaşmadığı saptandı. Sosyal sağlık toplam skoru hariç tüm ölçeklerde AAA olan çocuklar ve ebeveynlerinin PedsQL4.0 değerlendirmeleri arasında anlamlı korelasyon olduğu saptandı. Demografik değişkenler ve klinik bulgular ile çocuk PedsQL4.0 arasında anlamlı ilişki saptanmadı.

Sonuç: Ailevi Akdeniz ateşi olan olgularda ölçek skorları istatistiksel anlamlı olmasa da sağlıklı kontrollere göre daha düşüktür. Çalışmamızda göreceli olarak az sayıda hasta olduğu göz önünde bulundurulduğunda bu alanda daha kapsamlı ve fazla sayıda hasta içeren çalışmalara ihtiyaç olduğu sonucuna varılmıştır.

Keywords

Çocuklar, Ailevi Akdeniz Ateşi, Yaşam kalitesi, Ebeveyn

Health Related Quality of Life of Children Aged 2-18 Years With Familial Mediterranean Fever

Abstract

Objective: We aimed to evaluate both child-self reported and parents proxy reported health related quality of life of children with familial Mediterranean fever (FMF) aged between 2-18 years old and to compare the scores with their healthy peers.

Material and Methods: Fifty -one patients with FMF and fifty one gender and age matched controls were enrolled in the study. Children aged 8-18 years completed the PedsQL4.0 child form questionnaires. Parents of all cases completed the PedsQL4.0 parent form.

Results: Lower scores in the FMF group, with no statistical significance, was found between the FMF cases and healthy volunteers aged 8-18 years for the physical health, social health, school functioning, psychosocial total and scale total score of PEDsQL4.0 child self-report. The parent proxy report PedsQL4.0 scores of all patients with FMF were lower than the healthy group for physical, emotional, social, psycho-social, school functioning scores and scale total score but the difference was not statistically significant. A significant correlation was present between PedsQL4.0 child self-report and parent PedsQL4.0 report in all subscales except for social health total score. There was not a significant correlation between the demographic variables and clinical features of the patients and the child subscales of PedsQL4.0.

Conclusion: The scores of FMF cases from the scales were lower than those of the healthy volunteers from the questionnaires but this difference was not statistically significant. Considering the relatively small sample size of the study it is obvious that more comprehensive prospective studies are required on this subject.

Keywords

Children, Familial Mediterranean fever, Quality of life, Parent

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