Morgagni-Steawart-Morel syndrome: Case report

Year 2019, , 434 - 436, 30.09.2019

Emrah Doğan , Marwa Mouline

https://doi.org/10.18663/tjcl.453912

Cited By: 1

Abstract

Hyperostosis frontalis interna (HOFI) is characterized
by the benign growth of the inner plate of the frontal bone. It is most common
in older women. Etiology is unknown. Morgagni-Stewart-Morel syndrome(MSM) is
characterized by HOFI, obesity, hirsutism and mental illnesses but these
associations are mostly based only on case reports. MSM syndrome is misunderstood
and less reported pathology. The clinical presentation is not well defined andits
finding is usually coincidental. The patient may present variable
symptomatology. The idea that we should keep in mind is that HOFI representthe
main pattern of MSM. Thus, it is highly importantto specify the presence and
degree of HOFI in radiological reports.

Keywords

Morgagni-Stewart-Morel Syndrome, Hiperostosis frontalis interna

Morgagni-Steawart-Morel sendromu: Olgu sunumu

Abstract

Hiperostozis frontalis interna(HOFI) frontal
kemiğin iç tabulasının iyi huylu büyümesi ile karakterizedir. En sık yaşlı
kadınlarda görülür. Etiyoloji bilinmemektedir. Morgagni-Stewart-Morel sendromu (MSM);
HOFI, obezite, hirsutizm ve zihinsel rahatsızlıklar ile karakterizedir ancak bu
ilişkiler çoğunlukla vaka raporlarına dayanır. MSM sendromu daha az anlaşılan ve
bildirilen sendromdur. Hasta çeşitli semptomlar gösterebilir. HOFI’nin MSM’nin bir
paterni olduğu akılda tutulmalıdır. Radyolojik raporlamada bu nedenle HOFI
varlığını ve derecesini belirtmek önem teşkil eder. 

Keywords

Morgagni-Stewart-Morel Sendromu, Hiperostozis frontalis interna

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