Lymphangioleiomyomatosis-associated spontaneous tension hemopneumothorax in multiple organ involvement tuberculosis

Year 2019, , 430 - 433, 30.09.2019

Bayram Metin , Mustafa Fatih Erkoç , Sevinç Şahin , Yavuz Selim İntepe

https://doi.org/10.18663/tjcl.477832

Abstract

Tuberosclerosis
complex  is a genetic disorder that can
affect several organs (such as the brain, lungs kidneys, eyes, the heart, bones
and the skin). Pulmonary lymphangioleiomyomatosis is a disease that is mostly
seen among young adult women. It is characterized primarily by the
non-neoplastic atypical proliferation of smooth muscle cells in the lung
parenchyma. Here, we present a case of lymphangioleiomyomatosis-associated
spontaneous hemopneumothorax in a tuberosclerosis patient, which we did not
encounter in the literature.

Keywords

tuberoussclerosis, lymphangioleiomyomatosis, hemopneumothorax

Multi organ tutulumlu tüberosklerozda lenfanjiyoleiyomiyomatozise bağlı spontan tansiyon hemopnömotoraks olgusu

Abstract

Tuberosklerozis kompleksi, beyin, akciğer, böbrek,
göz, kalp, kemik ve deri gibi organları etkileyebilen genetik bir hastalıktır. Pulmoner
lenfanjiyoleiyomiyomatozis daha çok genç erişkin bayanlarda görülen bir
hastalıktır. Akciğer parankimindeki düz kas hücrelerinin neoplastik olmayan
atipik proliferasyonu ile karakterizedir. Biz burada literatürde
karşılaşmadığımız tuberosklerozis hastasında lenfanjiyoleiyomiyomatozise bağlı
spontan hemopnömotoraks olgusunu sunuyoruz.

Keywords

tuberosklerozis, lenfanjiyoleiyomiyomatozis, hemopnömotoraks

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