Intramedullary Schwannomas: A Rare Case Report

Yıl 2024, Cilt: 50 Sayı: 3, 557 - 560, 12.01.2025

Ali İmran Özmarasalı , Pınar Eser Ocak , Mine Özşen , Şeref Doğan

https://doi.org/10.32708/uutfd.1486611

Öz

This case report aims to review a very rare case of intramedullary schwannoma with literature review. A 52-year-old male patient presented with complaints of difficulty walking and leg spasms. Radiological examinations revealed an intradural lesion at the C7-T3 level, and gross total resection was performed. No postoperative neurological deterioration was observed. The patient's preoperative ASIA and McCormick scores were recorded as C and 3, respectively; while they were recorded as 6th months and 1st year D, E and 2, 1 postoperatively, respectively. Histopathological examination reported schwannoma. Our patient has been under outpatient clinic follow-up for four years. Intramedullary schwannoma is a rare spinal cord tumor with 198 cases reported in the literature. The exact etiopathogenesis of this rare condition is still under debate. Due to the low recurrence rate, microsurgical gross total excision is the gold standard in the treatment of intramedullary schwannomas.

Anahtar Kelimeler

Schwannomas, Intramedullary, Spinal cord, Intradural Tumors

İntramedüller Schwannoma: Nadir Olgu Sunumu

Öz

Bu olgu sunumu, oldukça nadir görülen intramedüller yerleşimli schwannoma olgusunun literatür eşliğinde incelenmesini amaçlamaktadır. 52 yaşında erkek hasta, yürüme güçlüğü ve bacaklarda kasılma şikayetiyle başvurdu. Radyolojik incelemelerde C7-T3 seviyesinde intradural yerleşimli kitlesel lezyon saptanması üzerine gross total rezeksiyon yapıldı. Postoperatif nörolojik kötüleşme gözlenmedi. Hastanın ameliyat öncesi ASIA ve McCormick skorları sırasıyla C ve 3, ameliyat sonrası ise sırasıyla 6. ay ve 1. yılda D, E ve 2, 1 olarak kaydedildi. Histopatolojik inceleme, schwannoma olarak rapor edildi. Hastamız 4 yıldır poliklinik takibimizdedir. İntramedüller schwannoma, literatürde 198 vaka bildirilen nadir bir omurilik tümörüdür. Bu nadir durumun kesin etyopatogenezi konusunda tartışmalar devam etmektedir. Düşük nüks oranı nedeniyle intramedüller schwannomaların tedavisinde altın standart mikroşirurjikal gross total eksizyondur.

Anahtar Kelimeler

Schwannomas, Intramedullary, Spinal cord, Intradural Tumors

Kaynakça

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