VULVAR PARAURETRAL EKSTRAGASTROINTESTİNAL STROMAL TUMOR; A CASE REPORT

Year 2017, Volume: 48 Issue: 4, 168 - 172, 07.12.2017

Mesut Tek , İdris Aydın Yasemin Yuyucu Karabulut Mürşide Çevikoğlu Kıllı

https://doi.org/10.16948/zktipb.290910

Abstract

SUMMARY

Gastrointestinal
Stromal Tumors (GISTs) are mesenchymal tumors that are arises from the wall of
the gastrointestinal tract and is throught to originate from the Interstitial
Cells of Cajal (ICC), which regulate the motility of the gastrointestinal
tract. More rarely neoplasms with histology and immunohistochemistry similar to
gastrointestinal stromal tumors may ocur outside the gastrointestinal tract and
are so-called Extra-gastrointestinal Stromal Tumors (EGISTs). Surgical removal  is the gold standard treatment for
non-metastatic Extragastrointestinal stromal tumors. We reported a very rare
case of ekstragastrointestinal stromal tumor arising from the vulva in this
article.

Keywords

EKSTRA GASTROINTESTINAL STROMAL TUMOR, GASTROINTESTINAL STROMAL TUMOR, PARAURETRAL MASS, VULVAR MASS

VULVADA PARAÜRETRAL EKSTRAGASTROİNTESTİNAL STROMAL TÜMÖR; OLGU SUNUMU

Abstract

ÖZET

Gastrointestinal
Stromal Tümörler (GİST), gastrointestinal sistem duvarı peristaltizmini düzenleyen
İnterstisyel Cajal Hücreleri’nden (İCH) kaynaklandığı düşünülen mezenkimal
tümörlerdir. Ekstragastrointestinal  Stromal
Tümörler (EGİST) daha nadir görülen, histoloji ve immünohistokimlyasal açıdan
gastrointestinal stromal tümörler ile benzer ancak gastro intestinal yolak
dışında oluşan tümörlerdir. Metastatik olmayan ekstragastrointestinal stromal
tümörlerin cerrahi olarak çıkarılması altın standart tedavidir. Bu makalede,
nadiren vulvadan köken alan ekstragastrointestinal stromal tümörlü bir olgu
sunduk.

Keywords

EKSTRA GASTROİNTESTİNAL STROMAL TÜMÖR, GASTROİNTESTİNAL STROMAL TÜMÖR, PARAÜTERRAL KİTLE, VULVAR KİTLE

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