FİBRÖZ DİSPLAZİ: DERLEME

Yıl 2020, Cilt: 30 Sayı: 2, 312 - 319, 15.04.2020

Muhammed Enes Naralan , Fatma Çağlayan Furkan Cantürk Esin Akol Görgün

https://doi.org/10.17567/ataunidfd.658046

Cited By: 1

Öz

Fibröz displazi (FD), normal kemik dokusunun fibröz dokuyla yer değiştirmesi sonucu oluşan fibro-osseoz bir lezyondur. Vücutta kraniyofasiyal kemiklerde olabileceği gibi diğer kemiklerde de görülebilir. FD, tek bir kemikte tutulum gösteriyorsa monostotik fibröz displazi (MFD), birden fazla kemikte tutulum gösteriyorsa poliostotik fibröz displazi (PFD) adını almaktadır. Ayrıca genel sistemik etkileri olan McCune-Albright sendromunun (MAS) bir komponenti olarak da görülebilmektedir. Tedavisinde, takipten cerrahi rezeksiyona kadar birçok yol izlenebilmektedir. Bu makalede FD’nin etiyolojisi, klinik davranışları, histopatolojisi, radyolojik özellikleri, ayırıcı tanısı ve tedavisi hakkında detaylı bilgi verilmiştir.
Anahtar kelimeler: Fibröz displazi, McCune-Albright Sendromu, Monostotik fibröz displazi, Poliostotik fibröz displazi
Fibrous Dysplasia: Review
Abstract
Fibrous dysplasia (FD) is a fibro-osseous lesion caused by the replacement of normal bone tissue with fibrous tissue. It can be seen in craniofacial bones in the body or in other bones. If FD shows involvement in a single bone, monostotic fibrous dysplasia (MFD) is referred to as polyostotic fibrous dysplasia (PFD), if it shows involvement in more than one bone. It can also be seen as a component of McCune-Albright syndrome (MAS) with general systemic effects. In the treatment, many paths can be followed up from follow-up to surgical resection. In this article, detailed information about etiology, clinical behavior, histopathology, radiological features, differential diagnosis and treatment of FD are given.
Key Words: Fibrous Dysplasia, McCune-Albright Syndrome, Monostotic Fibrous Dysplasia, Polyostotic Fibrous Dysplasia

Anahtar Kelimeler

Fibröz displazi, McCune-Albright Sendromu, Monostotik fibröz displazi

Kaynakça

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