Böbreğin oldukça nadir görülen çocukluk çağı tümörü, Renel Clear Cell Sarkom: Olgu Sunumu

Yıl 2016, Cilt: 6 Sayı: 1, 35 - 37, 19.10.2016

Tamer Sekmenli İlhan Çiftci , Yavuz Koksal

https://doi.org/10.16899/ctd.90769

Öz

Böbreğin Clear-cell Sarkomu çocukların primer malign tümörlerinin yaklaşık %3’ünün oluşturur ve nadir görülen bir tümördür. Kemiklere metastaz yapması ve kötü prognoza sahip olması nedeni ile saldırgan bir tümör olarak bilinir. Klinik ve radyolojik olarakWilms’ Tümörüne benzer. Karın sol boşluğunda yerleşen 12 yaşında olguyu sunduk.

Anahtar Kelimeler

Clear Cell Sarkom, Wilms Tümörü, Çocuk.

Extremely Rare Childhood Tumor, Renal Clear Cell Sarcoma: A Case Report

Öz

Clear-cell sarcoma of the kidney (CCSK) is a rare tumor and comprises 3% of primary pediatric malignant renal tumors.  It is known as an aggressive tumor that metastases to the bones with a poor prognosis.  Clinically and radiologically, it can mimic Wilms' tumor. We present a CCSK case in the left abdominal area in a 12 year old patient.

Anahtar Kelimeler

Clear cell sarcoma; Wilms tumor; Child

Kaynakça

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