Dalak ve Karaciğer Tutulumu ile Seyreden T Hücre/ Histiyositten Zengin B Hücreli Lenfoma Olgusu

Yıl 2017, Cilt: 9 Sayı: 4, 304 - 309, 01.12.2017

Ayşe Kevser Demir , Ayşe Kefeli Ali Akın , Şafak Şahin Eda Albayrak Sedanur Kurban Memiş Hilmi Atay

Öz

T hücre/Histiyositten zengin B hücreli lenfoma (TC/HRBCL), diffüz büyük
B-hücreli lenfoma (DBBHL)’nin son zamanlarda tanınmış morfolojik bir
varyantıdır. DLBCL’lerin %2’den azını oluşturur. Diğer DLBCL alt tiplerine göre
daha erken yaşlarda görülür ve sıklıkla erkek bireyler etkilenir. Bu sunumda
diffüz karaciğer ve dalak tutulumu olan TC/HRBCL tanısı almış otuz üç yaşında
erkek bir olgunun klinik ve radyolojik bulgularının sunumu yapılmaktadır.

Anahtar Kelimeler

T hücre/Histiyositten zengin B hücreli lenfoma, karaciğer tutulumu

T-Cell/Histiocyte-Rich B-Cell Lymphoma with Spleen and Liver Involvement

Öz

T-Cell/Histiocyte-Rich B-Cell Lymphoma (TC/HRBCL) is a recently recognized
morphological variant of diffuse large B-cell lymphoma (DBBHL). It is compose
of less than 2% of DLBCLs. It is seen at earlier ages than other DLBCL subtypes
and is often affected by male subjects. In this presentation, we present
clinical and radiological findings of a thirty-three-year-old male patient with
a diagnosis of TC/HRBCL with diffuse liver and spleen involvement.

Anahtar Kelimeler

T-Cell/Histiocyte-Rich B-Cell Lymphoma, liver involvement

Kaynakça

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