66 Yaşında Kadın Hastada Yeni Tanı ALCAPA Sendromu

Yıl 2020, Cilt: 46 Sayı: 2, 221 - 224, 01.08.2020

Murat Kerkütlüoğlu , Enes Çelik , Bayram Öztürk , Hakan Güneş

https://doi.org/10.32708/uutfd.705221

Öz

Sol koroner arterin pulmoner arterden (ALCAPA) anormal kökeni, nadir görülen doğuştan kalp anomalisidir. Genellikle klinik seyir; ileri sol kalp yetmezliği ve yaşamın ilk aylarında ortaya çıkan mitral kapak yetersizliğidir. Bununla birlikte, bazı durumlarda sağ koroner arterden oluşan kollateraller miyokard perfüzyonu için yeterlidir. ALCAPA'lı hastalarda aritmi veya erişkin yaşamda ani kalp ölümü ilk klinik başvuru olabilir. Göğüs ağrısı ve çarpıntı şikayetleri ile acil servise başvuran ve sol koroner arterde anormal köken saptanan 66 yaşında kadın hastayı sunmaktayız.

Anahtar Kelimeler

L-ALCAPA, koroner anomali, kardiyak arrest, yetişkin

New Diagnosis ALCAPA Syndrome in a 66-Year-Old Woman

Öz

Abnormal origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital heart anomaly. Usually the clinical course; advanced left heart failure and mitral valve insufficiency that occurs in the first months of life. However, in some cases collaterals consisting of the right coronary artery are sufficient for myocardial perfusion. Arrhythmia or sudden cardiac death in adult life may be the first clinical presentation in patients with ALCAPA. We present a 66-year-old female patient who was admitted to the emergency department with complaints of chest pain and palpitations and was found to have an abnormal origin in the left coronary artery.

Anahtar Kelimeler

L-ALCAPA, coronary anomaly, cardiac arrest, adult

Kaynakça

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